Herlyn-Werner-Wunderlich Syndrome: Report of a Prenatally Recognised Case and Review of the Literature

• Tipo: Outra Publicação em Revista Científica Internacional
• Data: 2019

Autores

Tuna T (Autor) FMUP; Estevão-Costa J (Autor) FMUP; Ramalho C (Autor) FMUP; Fragoso AC (Autor) FMUP

Revista

Título: Urology

Vol. 125

Páginas: 205-209

ISSN: 0090-4295

Editora: Elsevier

Indexação

ISI Web of Knowledge - 17 Citações

ISI Web of Science

Scopus - 28 Citações

Pubmed / Medline

Classificação Científica

CORDIS: Ciências da Saúde > Ciências Médicas > Medicina

Outras Informações

ID Authenticus: P-00Q-3AG

DOI: 10.1016/j.urology.2018.12.022

Abstract (EN): Herlyn-Werner-Wunderlich syndrome, defined by the triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis, is a rare Mullerian malformation, usually diagnosed after menarche, when symptoms related to hematocolpos arise. Rarely, this malformation is diagnosed in the neonatal period, normally following prenatal diagnosis of renal agenesis. Herein, a case recognized on prenatal imagiology that underwent surgery on the fourth day of life is reported. The records of prepubertal cases were also collected, addressing the clinical and imagiological features. In the presence of a solitary kidney and/or a pelvic mass on prenatal ultrasound, Herlyn-Werner-Wunderlich syndrome should be considered, enabling neonatal treatment. (c) 2018 Elsevier Inc.

Idioma: Inglês

Tipo (Avaliação Docente): Científica

Nº de páginas: 5