CONGENITAL PULMONARY LYMPHANGIECTASIA AND CHYLOTHORAX - A CASE SERIES

• Tipo: Artigo em Revista Científica Internacional
• Data: 2017

Autores

Rocha, G (Autor) Outra; Soares, P (Autor) Outra; Inês Azevedo (Autor) FMUP; Baptista, MJ (Autor) Outra; Casanova, J (Autor) Outra; Moura, CS (Autor) Outra; Guimaraes, H (Autor) Outra

Revista

Título: Lymphology

Vol. 50

Páginas: 188-196

ISSN: 0024-7766

Editora: International Society of Lymphology

Indexação

ISI Web of Knowledge - 2 Citações

Scopus - 5 Citações

Outras Informações

ID Authenticus: P-00N-VJ2

Abstract (EN): Congenital pulmonary lymphangiectasia (CPL) and chylothorax (CC) are rare lymphatic developmental disorders. We report six clinical cases of CPL and CC that were admitted to our level III neonatal intensive care unit over the last 20 years. One case of unilateral CC was successfully treated with pleuro-amniotic shunt; three cases of bilateral CC were associated to lung hypoplasia, hydrops fetalis, and generalized lymphangiectasias; one case of CPL was associated with obstructive congenital heart defect; one case of unilateral CC was successfully treated with thoracocentesis and medium-chain triglyceride diet. Mortality was high (66.6%).

Idioma: Inglês

Tipo (Avaliação Docente): Científica

Nº de páginas: 9