Annular pancreas: Unusual presentation of a rare malformation [Pâncreas anular: Apresentação pouco habitual de uma malformação rara]

• Tipo: Artigo em Revista Científica Nacional
• Data: 2019

Autores

Fortuna J (Autor) Outra; Rodrigues AL (Autor) Outra; Amante S (Autor) Outra; Estevão-Costa J (Autor) FMUP; Fragoso AC (Autor) FMUP

Revista

Título: Portuguese Journal of Pediatrics

ISSN: 2184-3333

Editora: Portuguese Society of Paediatrics

Indexação

Scopus - 0 Citações

Pubmed / Medline

Classificação Científica

CORDIS: Ciências da Saúde > Ciências Médicas > Medicina

Outras Informações

ID Authenticus: P-00T-J3H

DOI: 10.25754/pjp.2019.14168

Abstract (EN): A case of a 6-month-old female infant presenting post-prandial vomiting and poor weight gain is presented. She was malnourished and dehydrated with no abdominal distension or neurological signs. Laboratory testing revealed hypochloremic hypokalemic alkalosis. After the exclusion of infectious disease and food intolerance, plain abdominal X-rays revealed a ¿double bubble¿ sign with distal air, thereby suggesting partial duodenal obstruction. An upper gastrointestinal contrast study confirmed this diagnosis. She was then referred to a tertiary hospital for surgical treatment. At surgery, a duodenum-duodenostomy was performed due to a complete annular pancreas, with an excellent outcome. Annular pancreas is a rare entity. When symptoms arise, they usually occur in the neonatal period. As the present case illustrates, it may be symptomatic at later ages, requiring a high grade of suspicion in order to diagnose and treat it early.

Idioma: Inglês

Tipo (Avaliação Docente): Científica