Congenital lobar emphysema of the newborn. Report of four clinical cases

• Type: Article in International Scientific Journal
• Date: 2010

Authors

Rocha, G (Author) Other; Inês Azevedo (Author) FMUP; Pinto, JC (Author) Other; Moura, CS (Author) Other; Guimarães H (Author) FMUP

Journal

Title: Revista Portuguesa de Pneumologia

Vol. 16 No. 2

Pages: 849-857

ISSN: 0873-2159

Publisher: Sociedade Portuguesa de Pneumologia

Indexing

ISI Web of Knowledge - 1 Citation

Scopus - 3 Citations

Pubmed / Medline

Scientific classification

FOS: Medical and Health sciences > Other medical sciences

CORDIS: Health sciences > Medical sciences > Medicine

Other information

Authenticus ID: P-003-3TH

DOI: 10.1016/s2173-5115(10)70083-x

Abstract (EN): Introduction: Congenital lobar emphysema (CLE) is a rare anomaly of lung development that presents in the neonatal period in about 50% of the cases. The authors report four clinical cases of congenital lobar emphysema in the newborn. Clinical cases: Four term newborns, 3M/ 1F, were admitted for respiratory distress starting between 20 hours of life and 18 days. The chest x-ray at admission was suggestive of CLE and the diagnosis was confirmed by computorized tomography. The CLE affected the right upper lobe in three cases and the medium lobe in one case. All patients were treated with lobectomy. The pathological study of the surgical specimens confirmed the diagnosis in the four cases, and revealed hypoplasia of the bronquiolar tree cartilage in three. Conclusions: Our series is according to literature regarding to male gender preponderance, clinical presentation, different time to diagnosis, unilobar involvement and no identification of an evident aetiology in one case. Surgical treatment was universal.

Language: Portuguese

Type (Professor's evaluation): Scientific

No. of pages: 9