Targeting specific nutrient deficiencies in protein-restricted diets: some practical facts in PKU dietary management

• Type: Article in International Scientific Journal
• Date: 2014

Authors

Filipa B Pimentel (Author) Other; Rita C Alves (Author) Other; Teresa T Oliva Teles (Author) Other; Anabela S G Costa (Author) Other; Telmo J R Fernandes (Author) Other; Manuela F Almeida (Author) Other; Duarte Torres (Author) FCNAUP; Cristina Delerue Matos (Author) Other; Beatriz. B P P Oliveira (Author) FFUP

Journal

Title: Food and Function

Vol. 5

Pages: 3151-3159

ISSN: 2042-6496

Publisher: Royal Society of Chemistry

Indexing

ISI Web of Knowledge - 3 Citations

ISI Web of Science

Scopus - 3 Citations

Scientific classification

FOS: Agrarian Sciences > Other Agrarian Sciences

CORDIS: Health sciences

Other information

Authenticus ID: P-00A-16W

DOI: 10.1039/c4fo00555d

Abstract (EN): Among aminoacidopathies, phenylketonuria (PKU) is the most prevalent one. Early diagnosis in the neonatal period with a prompt nutritional therapy (low natural-protein and phenylalanine diet, supplemented with phenylalanine-free amino acid mixtures and special low-protein foods) remains the mainstay of the treatment. Data considering nutrient contents of cooked dishes is lacking. In this study, fourteen dishes specifically prepared for PKU individuals were analysed, regarding the lipid profile and iron and zinc contents. These dishes are poor sources of essential nutrients like Fe, Zn or n-3 fatty acids, reinforcing the need for adequate supplementation to cover individual patients' needs. This study can contribute to a more accurate adjustment of PKU diets and supplementation in order to prevent eventual nutritional deficiencies. This study contributes to a better understanding of nutrient intake from PKU patients' meals, showing the need for dietary supplementation.

Language: English

Type (Professor's evaluation): Scientific

Notes: <a href="http://gateway.isiknowledge.com/gateway/Gateway.cgi?GWVersion=2&SrcAuth=Alerting&SrcApp=Alerting&DestApp=WOS&DestLinkType=FullRecord&KeyUT=000345454700011">Indexado na ISI Web of Science</a>

No. of pages: 9