Hepatic perivascular epithelioid tumor (PEComa). A case report

• Type: Article in International Scientific Journal
• Date: 2017

Authors

Cardoso, H (Author) Other; Silva, M (Author) Other; Vilas Boas, F (Author) Other; Cunha, R (Author) Other; Lopes, J (Author) Other; Maia, JC (Author) Other; Macedo G (Author) FMUP

Journal

Title: Clinics and Research in Hepatology and Gastroenterology

Vol. 41

Pages: E43-E46

ISSN: 2210-7401

Publisher: Elsevier

Indexing

ISI Web of Knowledge - 6 Citations

Other information

Authenticus ID: P-00N-29H

DOI: 10.1016/j.clinre.2017.02.003

Abstract (EN): A 37-year-old female had liver nodules found in an abdominal ultrasound scan. The radiological features were suggestive of hepatocellular adenomas, although there were some atypical findings. Two years later, one of the nodules showed dimensional progression and intralesional hemorrhage. The patient underwent a left hepatectomy and the postoperative course was uneventful. The histological exam and the immunohistochemistry were consistent with the diagnosis of PEComa. The PEComa is a mesenchymal tumor rarely described in the liver. The preoperative diagnosis of PEComa is very difficult and, with this report, the authors intend to increase the limited knowledge relating to natural history and optimal treatment of this rare condition.

Language: English

Type (Professor's evaluation): Scientific

No. of pages: 4