Epithelioid sarcoma of the spine: Case report and literature review

• Type: Another Publication in an International Scientific Journal
• Date: 2014

Authors

Chamadoira, C (Author) Other; Paulo Pereira (Author) FMUP; Silva, PS (Author) FMUP; Castro, L (Author) Other; Vaz, R (Author) Other

Journal

Title: Neurocirugia

Vol. 25

Pages: 179-182

ISSN: 1130-1473

Publisher: Sociedad Espanola de Neurocirugia

Indexing

ISI Web of Knowledge - 5 Citations

Scopus - 4 Citations

Other information

Authenticus ID: P-009-MZ0

DOI: 10.1016/j.neucir.2014.01.001

Abstract (EN): Epithelioid sarcomas are rare mesenchymal neoplasms mainly arising in the limbs of young adults. We report the case of a 24-year-old male presenting low back pain radiating to both lower limbs, constipation and urinary retention. The MRI scan showed an intraspinal lesion extending from L4 to 52. Surgery resulted in gross total removal of the extradural lesion and partial removal of the intradural component. The immunohistological study of the lesion was consistent with an epithelioid sarcoma. The patient was submitted to radiotherapy and chemotherapy, but a local recurrence of the lesion and dissemination along the neuraxis were observed 3 months after surgery. Despite treatment, the patient died 4 months after the surgical procedure due to multiorgan failure. Despite there being isolated reports of epithelioid sarcomas appearing in the spine, this is, to our knowledge, the first case with intradural extension.

Language: English

Type (Professor's evaluation): Scientific

No. of pages: 4