Annular pancreas: Unusual presentation of a rare malformation [Pâncreas anular: Apresentação pouco habitual de uma malformação rara]

• Type: Article in National Scientific Journal
• Date: 2019

Authors

Fortuna J (Author) Other; Rodrigues AL (Author) Other; Amante S (Author) Other; Estevão-Costa J (Author) FMUP; Fragoso AC (Author) FMUP

Journal

Title: Portuguese Journal of Pediatrics

ISSN: 2184-3333

Publisher: Portuguese Society of Paediatrics

Indexing

Scopus - 0 Citations

Pubmed / Medline

Scientific classification

CORDIS: Health sciences > Medical sciences > Medicine

Other information

Authenticus ID: P-00T-J3H

DOI: 10.25754/pjp.2019.14168

Abstract (EN): A case of a 6-month-old female infant presenting post-prandial vomiting and poor weight gain is presented. She was malnourished and dehydrated with no abdominal distension or neurological signs. Laboratory testing revealed hypochloremic hypokalemic alkalosis. After the exclusion of infectious disease and food intolerance, plain abdominal X-rays revealed a ¿double bubble¿ sign with distal air, thereby suggesting partial duodenal obstruction. An upper gastrointestinal contrast study confirmed this diagnosis. She was then referred to a tertiary hospital for surgical treatment. At surgery, a duodenum-duodenostomy was performed due to a complete annular pancreas, with an excellent outcome. Annular pancreas is a rare entity. When symptoms arise, they usually occur in the neonatal period. As the present case illustrates, it may be symptomatic at later ages, requiring a high grade of suspicion in order to diagnose and treat it early.

Language: English

Type (Professor's evaluation): Scientific