SYSTEMIC NODULAR PANNICULITIS IN A PATIENT WITH ALPHA-1 ANTITRYPSIN DEFICIENCY (PISS PHENOTYPE)

• Type: Article in International Scientific Journal
• Date: 1993

Authors

PINTO, AR (Author) Other; MACIEL, LS (Author) Other; Carneiro F (Author) FMUP; RESENDE, C (Author) Other; CHAVES, FC (Author) Other; FREITAS, AF (Author) Other

Journal

Title: Clinical and Experimental Dermatology

Vol. 18

Pages: 154-155

ISSN: 0307-6938

Publisher: Wiley-Blackwell

Indexing

ISI Web of Knowledge - 21 Citations

Scopus - 25 Citations

Other information

Authenticus ID: P-001-N9S

DOI: 10.1111/j.1365-2230.1993.tb01000.x

Abstract (EN): The association of alpha-1 antitrypsin deficiency (PiZ phenotype) with systemic nodular panniculitis has been well documented. Despite reports of cases of systemic nodular panniculitis associated with other alpha-1 antitrypsin deficiency phenotypes, it is still not known if this association is fortuitous rather than causal. We report a case of systemic nodular panniculitis associated with alpha-1 antitrypsin deficiency (PiSS phenotype), with clinico-pathological features similar to those reported in cases associated with the PiZ phenotype.

Language: English

Type (Professor's evaluation): Scientific

No. of pages: 2